This corrects the abnormal triangular shape of the forehead and increases the intracranial space in the anterior fossa. ... Study how the condition affects learning and behavior; ... Fronto-orbital surgery for metopic and unilateral coronal synostosis. Object. The use of sagittal springs with strip craniectomy may be recommended for sagittal synostosis if the child is younger than 5 months at the time of initial surgery. 2009 Sep. 20(5):1439-44. . The records of 36 consecutive children with metopic synostosis followed at one craniofacial center from 1978 to 1993 were reviewed and parental questionnaires were completed to establish the frequency of mental retardation, learning disabilities, and behavioral problems associated with this synostosis. Variations of endoscopic and open repair of metopic craniosynostosis. Craniosynostosis is when one or more of the special seams (sutures) in a baby's skull close earlier than normal. Children with metopic, unicoronal or lambdoid synostosis were much more likely to have a learning problem than children with the most common form of single-suture craniosynostosis – sagittal synostosis. Metopic craniosynostosis is a type of non-syndromic craniosynostosis that occurs when the metopic suture fuses before birth. 2010 May 1. Hum Mol Genet. Also known as cranial spring surgery. Surgical therapy for true metopic synostosis involves a fronto-orbital advancement which allows for widening the skull at the temporal fossa. This page from Great Ormond Street Hospital (GOSH) explains the causes, symptoms and treatment of metopic craniosynostosis (also … The purpose of this study was twofold: first, to assess the degree of developmental, educational, and behavioral problems in patients with nonsyndromic trigonocephaly and second, to establish whether patients with mild degrees of trigonocephaly had a lower frequency of such problems. Increased EFG- and PDGFalpha-receptor signaling by mutant FGF-receptor 2 contributes to osteoblast dysfunction in Apert craniosynostosis. Metopic craniosynostosis. The metopic suture begins at the nose and continues superiorly to meet the sagittal suture. J Craniofac Surg. Children with metopic, unicoronal and lambdoid synostosis tended to score lower on most measures than those with sagittal fusion (P<.001 to .82). The neurobehavioral morbidity of nonsyndromic trigonocephaly is incompletely understood. Miraoui H, Ringe J, Haupl T, Marie PJ. Children with operated metopic synostosis performed significantly worse on measures of motor functioning (g w = −.45), visuospatial skills (g w = −.32), attention (g w = −.50), executive functioning (g w = −.36), arithmetic ability (g w = −.37), and behavior (g w = −.34). Treatment involves releasing the suture and expanding and rounding out the upper face, forehead and skull. 19(9):1678-89. . 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